Congenital hepatic fibrosis

Also called CHF

Congenital hepatic fibrosis causes your liver to become tough and scarred. This can cause a number of problems including portal vein hypertension.

It is one of a group of conditions called fibrocystic liver conditions. Many people with congenital hepatic fibrosis will also have another of these conditions. You can find out more about the others here. It can also be linked to polycystic kidney disease.

If you have both congenital hepatic fibrosis and Caroli disease you might hear this called “Caroli syndrome”.

Congenital hepatic fibrosis is usually found in young children. But can be diagnosed in adults.

The treatment for congenital hepatic fibrosis is all about controlling symptoms. And managing the effects of the other problems it can cause.


On this page:

Quick summary  | Causes | Symptoms | Tests | Treatment | Living with congenital hepatic fibrosis